Ultra-wide Field Imaging of an Operated Macular Hole in Gyrate Atrophy
نویسندگان
چکیده
Medical records of a 46‐year‐old woman with bilateral myopia, gyrate atrophy, and history of night blindness were reviewed. The patient underwent macular hole surgery in the left eye 3 years back. The surgery consisted of pars plana vitrectomy (PPV), induction of posterior vitreous detachment (PVD), internal limiting membrane (ILM) peeling, and fluid‐air exchange. She had serum ornithine level of 784 nmole/ml and a best‐corrected visual acuity (BCVA) of 1/60 (with correcting lens of −7.25D) in the left eye preoperatively with early posterior subcapsular cataract and a large macular hole (diameter :1254 μm; Cirrus HD‐OCT, Carl Zeiss Meditec, Dublin, CA, USA) with round localized neurosensory retinal detachment at the posterior pole. At month 3 after the operation, 6/60 vision (with correcting lens of ‐8.00‐1.00×100) in the left eye was documented, which remained unchanged. Six months after the operation, she underwent cataract surgery with implantation of a posterior chamber intraocular lens in the capsular bag in the left eye. At the last follow up examination, 3 years after PPV, intraocular pressure in both eyes was normal, and there was no squint. BCVA was 6/9 in the right eye (with correcting lens of ‐9.00‐3.00×90) and 6/60 in the left eye (with correcting lens of −3D). Fundus examination showed typical coalescent areas of scalloped chorioretinal atrophy in both eyes [Figures 1 and 2]. Right eye had central macular thickness of 151 μm in optical coherence tomography (OCT, Cirrus HD‐OCT, Carl Zeiss Meditec, Dublin, CA, USA) without any evidence Ultra‐wide Field Imaging of an Operated Macular Hole in Gyrate Atrophy
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